- Uncommon, comprises ~1% of papillary urothelial neoplasms.
- Patients are typically <50 years old and can be seen in children.
- Often encountered as de novo lesion (without prior urothelial neoplasm).
- Cystoscopy shows a small unifocal papillary or elevated lesion.
- Recurrence rate of 9-31%, but with no risk for progression to higher-grade tumors.
* For any urothelial tumor to be called "papillary" the papillae should have a central fibrovascular core.